The main causes of death in Steinert disease

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Researchers have examined the causes of death in 1,021 patients with Steinert’s disease (or myotonic dystrophy type 1) in the United Kingdom.

– The main causes of death were cardiac (rhythm and conduction disorders) and respiratory (respiratory failure, inhalation pneumonitis, etc.), which are known complications of the disease.

– Although deaths from cancer appear to be increasing, they are no more frequent than in a control population.

The authors stress the importance of close, expert, multidisciplinary follow-up in this disease.

 

Mortality Trends and Causes of Death in Myotonic Dystrophy Type 1 Patients From the UK Clinical Practice Research Datalink Alsaggaf R, Pfeiffer RM, Pearce EE et al. Muscle Nerve. 2024 Dec

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