Researchers at the Centre de Référence des maladies neuromusculaires at Trousseau Hospital in Paris have studied data from patients with SMN1 type II-related proximal spinal muscular atrophy operated on for spinal deformity:
- the study included 25 patients operated on between 2009 and 2022 and divided into two groups,
- receiving either magnetic growth rods (MCGR type) (17/25) or posterior spinal arthrodesis (AVP) (9/25),
- surgery was performed on average slightly earlier in the MCGR group (9.7 years versus 12.6 years),
- correction of spinal deformity was slightly better with arthrodesis (55% vs. 44%),
- surgery was well tolerated (no need for blood transfusions, and identical impact on vital capacity pre- and post-operatively).
The authors emphasise the value of fixation in combating pelvic obliquity.
